Specific codes in ICD-10 are unique alphanumeric designations used to identify and categorize diseases, disorders, and conditions. They consist of 3-5 characters, including both letters and numbers, that provide a high level of detail and specificity.
| Language | Translation |
|---|---|
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Disorders of sphingolipid metabolism and other lipid storage disorders |
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Anomalies du métabolisme des sphingolipides et autres anomalies du stockage des lipides |
| Level | Code | Title | |
|---|---|---|---|
| 1 | IV | Endocrine, nutritional and metabolic diseases | |
| 2 | E70-E90 | Metabolic disorders | |
| 3 | E75 | Disorders of sphingolipid metabolism and other lipid storage disorders |
| Code | Title | |
|---|---|---|
| E75.0 | GM2 gangliosidosis | |
| E75.1 | Other gangliosidosis | |
| E75.2 | Other sphingolipidosis | |
| E75.22 | Gaucher disease type 1 | |
| E75.3 | Sphingolipidosis, unspecified | |
| E75.4 | Neuronal ceroid lipofuscinosis | |
| E75.5 | Other lipid storage disorders | |
| E75.6 | Lipid storage disorder, unspecified |