OGSIVEO Film‑coated tablet Ref.[115825] Active ingredients: Nirogacestat

Source: European Medicines Agency (EU)  Revision Year: 2025  Publisher: SpringWorks Therapeutics Ireland Limited, Hamilton House, 28 Fitzwilliam Place, Dublin 2, D02 P283, Ireland

4.1. Therapeutic indications

Ogsiveo as monotherapy is indicated for the treatment of adult patients with progressing desmoid tumours who require systemic treatment.

4.2. Posology and method of administration

Ogsiveo should be initiated and monitored by a physician experienced in the use of anticancer therapies.

Posology

The recommended dose is 150 mg Ogsiveo twice daily, one dose in the morning and one dose in the evening. This dose should not be exceeded.

Duration of treatment

Ogsiveo should be continued until disease progression or unacceptable toxicity.

Missed dose

If a dose of Ogsiveo is missed, patients should not take an additional dose. Patients should take the next prescribed dose.

Dose adjustments for adverse reactions

The recommended dose modifications for selected adverse reactions are provided in Table 1.

For other severe adverse reactions, or in the event of life‑threatening adverse reactions, Ogsiveo should be withheld until the reaction is resolved to Grade ≤ 1 or baseline. Ogsiveo should only be restarted at a dose of 100 mg twice daily and only after carefully considering the potential benefit and likelihood of recurrence of the adverse reaction. Ogsiveo should be permanently discontinued for recurrence of severe or life-threatening adverse reaction upon rechallenge at the reduced dose.

Dose modifications should be made if patients experience the following adverse reactions (grades refer to Common Terminology Criteria for Adverse Events):

Table 1. Recommended dose modifications for adverse reactions in patients treated with Ogsiveo:

Adverse reactionRecommended action
Diarrhoea
Grade 3 diarrhoea persisting for ≥ 3 days
despite maximal medical therapy
Ogsiveo should be withheld until reaction is resolved to
Grade ≤ 1 or baseline, then it should be restarted at a
dose of 100 mg twice daily.
Skin reactions
Grade 3 folliculitisOgsiveo should be withheld until reaction is resolved to
Grade ≤ 1 or baseline, then it should be restarted at a
dose of 100 mg twice daily.
Grade 3 maculopapular rashOgsiveo should be withheld until reaction is resolved to
Grade ≤ 1 or baseline, then it should be restarted at a
dose of 100 mg twice daily.
Grade 3 hidradenitisOgsiveo should be withheld until reaction is resolved to
Grade ≤ 1 or baseline, then it should be restarted at a
dose of 100 mg twice daily.
Electrolyte abnormalities
Grade 3 hypophosphataemia persisting
for ≥ 7 days despite maximal
replacement therapy
Ogsiveo should be withheld until reaction is resolved to
Grade ≤ 1 or baseline, then it should be restarted at a
dose of 100 mg twice daily.
Grade 3 hypokalaemia despite maximal
replacement therapy
Ogsiveo should be withheld until reaction is resolved
to Grade ≤ 1 or baseline, then it should be restarted at a
dose of 100 mg twice daily.
Hepatic abnormalities
Alanine transaminase (ALT) or
Aspartate transaminase (AST) ≥ 3 to 5 x
ULN
Ogsiveo should be withheld until ALT, AST, or both are
resolved to < 3 x ULN or baseline, then it should be
restarted at a dose of 100 mg twice daily.
ALT or AST > 5 x ULNOgsiveo should be permanently discontinued.
Other adverse reactions
Anaphylaxis or other severe
hypersensitivity reaction
Ogsiveo should be permanently discontinued.

Special populations

Elderly population

No dose adjustment is recommended for patients who are aged 65 years or over. Clinical data in patients aged 65 years or over is limited.

Renal impairment

No dose adjustment is recommended in patients with mild or moderate renal impairment. Administration is not recommended in patients with severe renal impairment (see section 5.2).

Hepatic impairment

No dose adjustment is recommended in patients with mild or moderate hepatic impairment. Administration is not recommended in patients with severe hepatic impairment (see section 5.2).

Paediatric population

The safety and efficacy of Ogsiveo in children from 2 to 18 years of age have not been established. Ogsiveo should not be used in children from birth to less than 2 years of age because of potential safety concerns related to structural and functional growth. Currently available data are described in sections 4.8 and 5.1, but no recommendation on a posology can be made.

Method of administration

Ogsiveo is for oral use.

The tablets may be taken with or without food. Tablets should not be broken, chewed or crushed because there are no data currently available to support other methods of administration.

Patients should avoid consuming grapefruit and grapefruit juice while taking Ogsiveo (see section 4.5).

4.9. Overdose

Signs and symptoms

The symptoms of Ogsiveo overdose are expected to be an extension of its pharmacological actions and may include diarrhoea, nausea, vomiting, hypophosphataemia, elevated transaminases, and epistaxis.

Management of overdose

Due to the high level of protein binding, Ogsiveo is not expected to be dialyzable in patients with normal serum protein levels. In the event of an overdosage, treatment with Ogsiveo should be stopped and general supportive measures should be initiated.

6.3. Shelf life

2 years.

6.4. Special precautions for storage

Store below 25°C.

6.5. Nature and contents of container

Ogsiveo 50 mg film‑coated tablets:

HDPE bottle with child resistant closure and induction seal containing 120 or 180 tablets.

Ogsiveo 100 mg film‑coated tablets
Ogsiveo 150 mg film‑coated tablets:

Clear PVC/PVDC blisters with aluminium lidding containing 14 tablets. One pack contains 56 tablets in 4 blisters.

Not all pack sizes may be marketed.

6.6. Special precautions for disposal and other handling

Any unused medicinal product or waste material should be disposed of in accordance with local requirements.

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